Cutaneous purpura of Sjögren syndrome successfully treated with hydroxychloroquine
نویسندگان
چکیده
INTRODUCTION Sj€ ogren syndrome is a systemic autoimmune disease characterized by dry eyes (keratoconjunctivitis sicca) and dry mouth (xerostomia). Common cutaneous manifestations of Sj€ ogren syndrome include xerosis, annular erythema, hypergammaglobulinemic purpura, and immunologic inflammatory conditions such as vasculitis (leukocytoclastic and urticarial). The clinical manifestations of vasculitis depend on the degree of skin and blood vessel involvement and can range from petechiae to palpable purpura and widespread ecchymoses. The findings often occur on the leg. Here we present a case of Sj€ ogren syndrome in which the primary cutaneous manifestations were ulcerated ecchymotic plaques that did not respond to highdose prednisone but had an excellent response to hydroxychloroquine.
منابع مشابه
Primary Sjögren syndrome that initially presented with repeated hypergammaglobulinemic purpura after prolonged sitting
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